The cystic fibrosis prognosis used to be a very severe diagnosis that would often take the life of an infant within a few years. As you can see below, there have been a number of discoveries and advancements in the treatment of cystic fibrosis throughout recent history which have improved the quality of life and prognosis for those with cystic fibrosis.
Cystic fibrosis is an autosomal recessive trait. This means that a child must inherit the CF gene from BOTH parents. Otherwise, the child does not have the symptoms of cystic fibrosis. The parents of a child with cystic fibrosis are known as carriers. This means that, although they do not have the symptoms of cystic fibrosis, they have 1 gene with the cystic fibrosis trait.
Intestinal blockage occurs in 10-15% of patients with cystic fibrosis. However, incidence of intestinal obstruction has decreased throughout the years due to advances in the administration of treatment enzymes. With improved treatment plans, the key precursors of DIOS are poor compliance with enzyme treatments, changes in diet, and dehydration.
Although cystic fibrosis affects the pancreas, lungs, intestines, and sinuses, it does not affect the heart’s ability to love. Cystic fibrosis does not change the fact that having a relationship can be an important part of your life. But, there are certain considerations that you must be prepared for in the long road ahead.
Concerns for Dating with Cystic Fibrosis
46% of patients thought twice about starting a relationship because of CF.
It is important in any relationship to share your life and experiences with your partner. For people with cystic fibrosis, there is a unique aspect of your life that your partner will probably not be familiar with. Many people with cystic fibrosis have long and healthy relationships and have faced the same worries or concerns as you before.
Below, we have outlined a few words of wisdom from members of the cystic fibrosis community to guide you in the first steps of sharing all the details of your life with your partner.
Cystic fibrosis is classically a pediatric disease. This means that it presents and is diagnosed in infancy. Until fairly recently, cystic fibrosis would never be considered a diagnostic option for an adult presenting CF related symptoms. This is due to the fact that historically, untreated cystic fibrosis resulted in early mortality.
However, recent occurrences have manifested where cystic fibrosis has been diagnosed in adulthood. It usually involves unique mutations of the CFTR and can present itself in a number of ways.
Though there is still no comprehensive cure for cystic fibrosis, the treatment and management options have drastically improved the prognosis for people with cystic fibrosis, enabling them to lead long and full lives. CF principally affects the secretions in the body, thus affecting many different organs with mucus buildup. It is of the utmost importance that people with cystic fibrosis maintain a strict medication and treatment schedule to increase longevity.
The most immediate symptom of cystic fibrosis in the lungs is that it makes breathing more difficult. The buildup of mucus blocks the airways and lines the walls of the lungs, making it more difficult to draw oxygen from each breath. A common analogy to the way cystic fibrosis restricts lung function is that it feels like breathing through a straw.
There are many cystic fibrosis treatments for clearing heavy mucus from the lungs, the most commonly known and prevalent symptom of CF. This is responsible for the primary cause of mortality (80%) in people with cystic fibrosis; respiratory failure.
Advances in treatment and technology have increased the prognosis from early childhood to 40 years and beyond. Each generation benefits from the most modern advancements in medicine and this number continues to rise.
Keeping your AlteraⓇ Nebulizer System clean and disinfected is important in ensuring that your treatment is as effective as possible. It only takes one unsanitary piece of your handset to introduce further infections or irritants into your respiratory system.